Scimitar Syndrome or Halasz Syndrome
Published: 2022-06-23
Page: 45-49
Issue: 2022 - Volume 5 [Issue 1]
Hanane El-Mouden *
Department of Radiology, Hôpital d’Enfants Abderrahim Harouchi, Casablanca, Morocco.
Loubna Nashi
Department of Radiology, Hôpital d’Enfants Abderrahim Harouchi, Casablanca, Morocco.
Siham Salam
Department of Radiology, Hôpital d’Enfants Abderrahim Harouchi, Casablanca, Morocco.
Kamilia Chbani
Department of Radiology, Hôpital d’Enfants Abderrahim Harouchi, Casablanca, Morocco.
Dalal Laoudiyi
Department of Radiology, Hôpital d’Enfants Abderrahim Harouchi, Casablanca, Morocco.
Lahcen Ouzidane
Department of Radiology, Hôpital d’Enfants Abderrahim Harouchi, Casablanca, Morocco.
*Author to whom correspondence should be addressed.
Abstract
Scimitar syndrome or Felson's vein-lobar syndrome is a very rare condition characterized by a combination of cardiopulmonary abnormalities including abnormal right pulmonary venous return, most often located in the inferior vena cava.
We here report an original observation of a nine-month-old female infant who presented with acute dyspnea in an endemic period. Symptomatic treatment for bronchiolitis was initiated, without success, with persistent respiratory distress. The diagnosis was suspected on chest X-ray and confirmed on CT scan which showed a single large right pulmonary vein draining into the right atrium associated with dextrocardia and pulmonary sequestration.
Keywords: Pulmonary arterial hypertension, scimitar syndrome, cardiopulmonary anomalies