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We would like to present an interesting and rare case of a 16-year boy, with the background of Type 1 diabetes since the age of 11 years who presented with Diabetic Ketoacidosis (DKA). He had multiple admissions with DKA in the preceding two years and his liver function tests were found to be deranged during the last two presentations. This was further evaluated through various investigations and a diagnosis of Mauriac syndrome was made.
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